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A FAMILY WITH FACTOR XIII DEFICIENCY CASE REPORT AND LITERATURE REVIEW

Zuhair Al-Barazanchi

Basrah Journal of Surgery مجلة البصرة الجراحية
ISSN: 16833589 Year: 2006 Volume: 12 Issue: 1 Pages: 92
Publisher: Basrah University جامعة البصرة

Abstract

Factor XIII deficiency is a rare disorder of coagulation characteri-zed by moderate to severe bleeding tendency with increased susceptibility to intracranial hemorrhages, almost normal coagulation screening tests, clot lysis in 5 M urea solution & a tendency to abnormal wound healing. It is inherited as an autosomal recessive trait. However, acquired causes for its deficiency are rarely encountered. We describe here an inherited form of F XIII deficiency in two members (a boy & a girl) in a one family in Basrah.

Keywords

FACTOR XIII --- DEFICIENCY